Patients of von Willebrand disease
- Patient Serial No - 1
Age:
9
Sex:
female
Location:
dhaka
Clinical Features:
The patient had a history of spontaneous gum bleeding, easy bruising, and prolonged bleeding following trauma since 2 years of her age. Her birth history was unremarkable. Her vitals were within normal limit except tachycardia, and oral cavity was normal.
Biochemical Data:
hemoglobin (Hb) level at 8.8 g/dL 4 , platelet count: normal, , bleeding time (BT): 10 minutes, clotting time (CT): 15 min, Von Willebrand factor:Ag assay:t 1%,
treatement and management:
Symptomatic treatment includes : - desmopressin acetate and tranexamic acid - prophylactic therapy in minor surgery - Desmopressin nasal spray